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关键词:
- 血栓性血小板减少性紫癜 /
- 鉴别诊断 /
- ADAMTS13 /
- 外周血涂片
Abstract: Thrombotic thrombocytopenic purpura (TTP) needs to be considered when microvascular hemolytic anemia combined with thrombocytopenia, and active treatment should be taken as soon as possible to reduce the mortality of TTP.However, due to the complexity of the emergency department, it is necessary to identify the pseudo-TTP caused by systemic diseases to avoid unnecessary treatment.The PLASMIC scoring system can assist in the diagnosis of TTP because the ADAMTS13 activity can not be obtained immediately.In addition, peripheral blood smears and LDH values also contribute to diagnosis. -
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